Hirschsprung Disease Pediatric Procedure

Hirschsprung Disease Pediatric Surgical Treatment – Pectus Excavatum Los Angeles

Definition of Hirschsprung Disease

Hirschsprung disease is a congenital condition that affects the colon of newborns, infants, and older children. It is characterized by the absence of nerve cells in the muscles of part or all of the large intestine (colon), which prevents bowel movements (stool) from passing. This can lead to severe constipation, intestinal blockage, and can dangerously enlarge the colon. At Pacific Coast Pediatric Surgery, we are committed to providing specialized care for children suffering from this condition.

Symptoms of Hirschsprung Disease in Pediatric Patients

Signs in Newborns: Newborns may show signs of Hirschsprung disease within the first weeks of life, including failure to pass meconium within the first 48 hours after birth, bloating or a swollen belly, and vomiting.

Signs in Older Children: Symptoms in older children can include severe constipation, growth failure, lack of energy, and a bloated abdomen. Recognizing these symptoms early can lead to a sooner diagnosis and treatment.

Diagnosis of Hirschsprung Disease in Pediatric Patients

Anorectal Manometry: This test measures how the anal muscles are working. At our clinic, we utilize the latest technology to ensure accurate results.

Biopsy: A biopsy of the rectum may be the most definitive test for diagnosing Hirschsprung disease, where a small sample of tissue is taken to look for the absence of nerve cells.

Surgical Procedures for Hirschsprung Disease in Pediatric Patients

Surgery is the main treatment for Hirschsprung disease. At Pacific Coast Pediatric Surgery, we specialize in several surgical procedures designed to alleviate the condition and enhance the patient’s quality of life. The specific type of surgery often depends on the extent of the disease.

• Pull-through Procedure: This is the most commonly performed surgery, where the affected portion of the colon is removed, and the healthy part is pulled through and attached to the anus, allowing for normal bowel movements.
• Ostomy: In some cases, an ostomy may be necessary as a temporary measure to allow the intestines to heal.

Postoperative Care for Pediatric Patients with Hirschsprung Disease

Postoperative care is vital for ensuring a smooth recovery and minimizing the risk of complications. This includes monitoring for signs of infection, managing pain, and slowly reintroducing foods. Our team at Pacific Coast Pediatric Surgery provides comprehensive postoperative support, ensuring that each child’s recovery is as comfortable and effective as possible.

Complications of Pediatric Hirschsprung Disease Surgery

While surgery for Hirschsprung disease is generally successful, there are potential complications, such as infection, bowel obstruction, and issues with stool control. Our team closely monitors each child for signs of complications to address them promptly should they arise.

Long-term Outlook for Pediatric Patients with Hirschsprung Disease

The long-term outlook for most children with Hirschsprung disease is positive, especially when the condition is diagnosed and treated early. After successful surgery, most children can lead a normal life with normal bowel function. Our commitment at Pacific Coast Pediatric Surgery is to not only provide advanced surgical care but also to offer compassionate follow-up care to ensure the best outcomes for our young patients.

At Pacific Coast Pediatric Surgery, under the leadership of Dr. Philip K. Frykman, we are dedicated to providing a caring and supportive environment for children affected by Hirschsprung disease and their families. From diagnosis through treatment and beyond, our experienced team is here to guide you every step of the way, utilizing state-of-the-art surgical techniques and a deeply compassionate approach to care.

Hirschsprung Disease Pediatric Procedure

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